Miocardiopatías. Miocardiopatía hipertrófica
- García Campos, A. 1
- Pérez Domínguez, M. 1
- Díaz Fernández, B. 1
- González Juanetey, J.R. 1
- 1 Servicio de Cardiología. Hospital Clínico Universitario de Santiago de Compostela. Santiago de Compostela. La Coruña. España. CIBERCV
ISSN: 0304-5412
Ano de publicación: 2021
Título do exemplar: Enfermedades cardiovasculares (VIII)
Serie: 13
Número: 42
Páxinas: 2433-2446
Tipo: Artigo
Outras publicacións en: Medicine: Programa de Formación Médica Continuada Acreditado
Resumo
Cardiomyopathies are a heterogeneous group of pathologies which have in common involvement of the ventricular myocardium in absence of overload or coronary, valve, or congenital disease that justifies it. They can be classified according to their phenotype. Hypertrophic cardiomyopathy is defined by an increase in left ventricle parietal thickness and is frequently associated with outflow tract obstruction and systolic anterior motion of the mitral valve. Sudden death can be one of the symptoms of this disease and risk stratification is of vital importance for deciding on the need for implantation of an automated defibrillator, whose use has been the main cause of a reduction in mortality in these patients in recent decades.
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